ORO FACIAL MANIFESTATIONS OF ENCEPHALO-TRIGEMINAL ANGIOMATOSIS:A CASE REPORT AND REVIEW OF LITERATURESturge Weber Syndrome also called as encephalotrigeminal angiomatosis is a sporadically occurring neurocutaneous syndrome caused by persistence of transit

Abstract

Sturge Weber Syndrome also called as encephalotrigeminal angiomatosis is a sporadically occurring neurocutaneous syndrome caused by persistence of transitory primordial arteriovenous connection of the foetal intracranial vasculature. It is characterized by vascular malformation with capillary venous angiomas that involve face, choroid of eye and leptomeninges with resulting neurological and orbital manifestations.The diagnosis is usually considered in a child presenting with seizures and facial capillary malformation along the trigeminal nerve distribution.In this article a case of Sturge‑Weber syndrome associated with oral manifestations and review on literature is presented.